A case of adult-onset congenital hepatic fibrosis

T. Nozaki; N. Muraishi; S. Fuwa; Y. Onoda; M. Kamo; Y. Okajima; Y. Saida; K. Suzuki

A case of adult-onset congenital hepatic fibrosis

T. Nozaki, N. Muraishi, S. Fuwa, Y. Onoda, M. Kamo, Y. Okajima, Y. Saida, K. Suzuki

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Abstract

We report a case of adult-onset congenital hepatic fibrosis (CHF). The patient, who was a woman in her twenties, presented pancytopenia. Abdominal CT and MRI show mild dilation of intrahepatic bile duct, multiple renal cysts, and portal hypertension, such as splenomegaly, hepatic deformity, collateral vessels. CHF is an inherited disorder that belongs to the family of ductal plate malformation. CHF is rare disease, but we should know imaging findings of this.

Original language	English
Pages (from-to)	1108-1111
Number of pages	4
Journal	Japanese Journal of Clinical Radiology
Volume	56
Issue number	9
Publication status	Published - 2011 Sept 10
Externally published	Yes

ASJC Scopus subject areas

Radiology Nuclear Medicine and imaging

Cite this

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abstract = "We report a case of adult-onset congenital hepatic fibrosis (CHF). The patient, who was a woman in her twenties, presented pancytopenia. Abdominal CT and MRI show mild dilation of intrahepatic bile duct, multiple renal cysts, and portal hypertension, such as splenomegaly, hepatic deformity, collateral vessels. CHF is an inherited disorder that belongs to the family of ductal plate malformation. CHF is rare disease, but we should know imaging findings of this.",

author = "T. Nozaki and N. Muraishi and S. Fuwa and Y. Onoda and M. Kamo and Y. Okajima and Y. Saida and K. Suzuki",

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AU - Nozaki, T.

AU - Muraishi, N.

AU - Fuwa, S.

AU - Onoda, Y.

AU - Kamo, M.

AU - Okajima, Y.

AU - Saida, Y.

AU - Suzuki, K.

PY - 2011/9/10

Y1 - 2011/9/10

N2 - We report a case of adult-onset congenital hepatic fibrosis (CHF). The patient, who was a woman in her twenties, presented pancytopenia. Abdominal CT and MRI show mild dilation of intrahepatic bile duct, multiple renal cysts, and portal hypertension, such as splenomegaly, hepatic deformity, collateral vessels. CHF is an inherited disorder that belongs to the family of ductal plate malformation. CHF is rare disease, but we should know imaging findings of this.

AB - We report a case of adult-onset congenital hepatic fibrosis (CHF). The patient, who was a woman in her twenties, presented pancytopenia. Abdominal CT and MRI show mild dilation of intrahepatic bile duct, multiple renal cysts, and portal hypertension, such as splenomegaly, hepatic deformity, collateral vessels. CHF is an inherited disorder that belongs to the family of ductal plate malformation. CHF is rare disease, but we should know imaging findings of this.

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AN - SCOPUS:80053538968

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JO - Japanese Journal of Clinical Radiology

JF - Japanese Journal of Clinical Radiology

IS - 9

ER -

A case of adult-onset congenital hepatic fibrosis

Abstract

ASJC Scopus subject areas

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