Desmoid-type fibromatosis of the head and neck in children: A case report and review of the literature

Hidetaka Miyashita, Seiji Asoda, Tomoya Soma, Kanako Munakata, Masaki Yazawa, Taneaki Nakagawa, Hiromasa Kawana

Research output: Contribution to journalReview article

6 Citations (Scopus)

Abstract

Background: Desmoid-type fibromatosis is defined as an intermediate tumor that rarely occurs in the head and neck of children. There is no doubt as to the value of complete surgical excision for desmoid-type fibromatosis. However, in pediatric patients, surgeons may often be concerned about making a wide excision because of the potential for functional morbidity. Some studies have reported a lack of correlation between margin status and recurrence. Therefore, we discussed our findings with a focus on the state of surgical margins. Case presentation: We report an unusual case of a 9-month-old Japanese girl who prior to presenting at our hospital underwent debulking surgery twice with chemotherapy for desmoid-type fibromatosis of the tongue at another hospital. We performed a partial glossectomy and simultaneous reconstruction with local flap and achieved microscopic complete resection. We also reviewed available literature of pediatric desmoid-type fibromatosis in the head and neck. Conclusions: We described successful treatment for the refractory case of pediatric desmoid-type fibromatosis. The review results showed that some microscopic incomplete resections of tumors in pediatric patients with desmoid-type fibromatosis tended to be acceptable with surgical treatment.

Original languageEnglish
Article number173
JournalJournal of Medical Case Reports
Volume10
Issue number1
DOIs
Publication statusPublished - 2016 Jun 10

Fingerprint

Aggressive Fibromatosis
Fibroma
Neck
Head
Pediatrics
Glossectomy
Tongue
Neoplasms
Morbidity
Recurrence
Drug Therapy
Therapeutics

Keywords

  • Case report
  • Children
  • Decision-making
  • Desmoid
  • Fibromatosis
  • Head and neck
  • Tongue

ASJC Scopus subject areas

  • Medicine(all)

Cite this

Desmoid-type fibromatosis of the head and neck in children : A case report and review of the literature. / Miyashita, Hidetaka; Asoda, Seiji; Soma, Tomoya; Munakata, Kanako; Yazawa, Masaki; Nakagawa, Taneaki; Kawana, Hiromasa.

In: Journal of Medical Case Reports, Vol. 10, No. 1, 173, 10.06.2016.

Research output: Contribution to journalReview article

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