Endomyocardial fibrosis: missing tricuspid valve and Fontan-like circulation

Yasuyuki Shiraishi; Takashi Kono; Yoko Fujii-Nishimura; Masayuki Shimoda; Yoshihiko Ikeda; Kazuaki Nakajima; Takahiko Nishiyama; Nobuhiro Nishiyama; Mitsushige Murata; Yuichiro Maekawa; Motoaki Sano; Keiichi Fukuda

doi:10.1007/s00380-015-0792-8

Endomyocardial fibrosis: missing tricuspid valve and Fontan-like circulation

Yasuyuki Shiraishi, Takashi Kono, Yoko Fujii-Nishimura, Masayuki Shimoda, Yoshihiko Ikeda, Kazuaki Nakajima, Takahiko Nishiyama, Nobuhiro Nishiyama, Mitsushige Murata, Yuichiro Maekawa, Motoaki Sano, Keiichi Fukuda

Research output: Contribution to journal › Article › peer-review

1 Citation (Scopus)

Abstract

Endomyocardial fibrosis (EMF) is a progressive type of obliterative/restrictive cardiomyopathy characterized by fibrosis of the apical endomyocardium of the ventricles. Although the prognosis of EMF patients is poor in tropical regions, the exact clinical course and pathogenesis of patients with EMF are not known. Here, we report the rare case with EMF in the seventh decade, who showed the disappearance of papillary muscles, chordae tendineae, and part of the tricuspid valves due to massive right ventricular thrombus. Because of those unusual findings of the isolated RV involvement, we observed continuous forward pulmonary artery flow, as occurring in a Fontan circulation.

Original language	English
Pages (from-to)	1-4
Number of pages	4
Journal	Heart and Vessels
DOIs	https://doi.org/10.1007/s00380-015-0792-8
Publication status	Accepted/In press - 2016 Jan 8

Keywords

Endomyocardial fibrosis
Inflammation
Prognosis
Right ventricle thrombus

ASJC Scopus subject areas

Cardiology and Cardiovascular Medicine

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10.1007/s00380-015-0792-8

Cite this

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title = "Endomyocardial fibrosis: missing tricuspid valve and Fontan-like circulation",

abstract = "Endomyocardial fibrosis (EMF) is a progressive type of obliterative/restrictive cardiomyopathy characterized by fibrosis of the apical endomyocardium of the ventricles. Although the prognosis of EMF patients is poor in tropical regions, the exact clinical course and pathogenesis of patients with EMF are not known. Here, we report the rare case with EMF in the seventh decade, who showed the disappearance of papillary muscles, chordae tendineae, and part of the tricuspid valves due to massive right ventricular thrombus. Because of those unusual findings of the isolated RV involvement, we observed continuous forward pulmonary artery flow, as occurring in a Fontan circulation.",

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doi = "10.1007/s00380-015-0792-8",

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TY - JOUR

T1 - Endomyocardial fibrosis

T2 - missing tricuspid valve and Fontan-like circulation

AU - Shiraishi, Yasuyuki

AU - Kono, Takashi

AU - Fujii-Nishimura, Yoko

AU - Shimoda, Masayuki

AU - Ikeda, Yoshihiko

AU - Nakajima, Kazuaki

AU - Nishiyama, Takahiko

AU - Nishiyama, Nobuhiro

AU - Murata, Mitsushige

AU - Maekawa, Yuichiro

AU - Sano, Motoaki

AU - Fukuda, Keiichi

PY - 2016/1/8

Y1 - 2016/1/8

N2 - Endomyocardial fibrosis (EMF) is a progressive type of obliterative/restrictive cardiomyopathy characterized by fibrosis of the apical endomyocardium of the ventricles. Although the prognosis of EMF patients is poor in tropical regions, the exact clinical course and pathogenesis of patients with EMF are not known. Here, we report the rare case with EMF in the seventh decade, who showed the disappearance of papillary muscles, chordae tendineae, and part of the tricuspid valves due to massive right ventricular thrombus. Because of those unusual findings of the isolated RV involvement, we observed continuous forward pulmonary artery flow, as occurring in a Fontan circulation.

AB - Endomyocardial fibrosis (EMF) is a progressive type of obliterative/restrictive cardiomyopathy characterized by fibrosis of the apical endomyocardium of the ventricles. Although the prognosis of EMF patients is poor in tropical regions, the exact clinical course and pathogenesis of patients with EMF are not known. Here, we report the rare case with EMF in the seventh decade, who showed the disappearance of papillary muscles, chordae tendineae, and part of the tricuspid valves due to massive right ventricular thrombus. Because of those unusual findings of the isolated RV involvement, we observed continuous forward pulmonary artery flow, as occurring in a Fontan circulation.

KW - Endomyocardial fibrosis

KW - Inflammation

KW - Prognosis

KW - Right ventricle thrombus

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SN - 0910-8327

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Endomyocardial fibrosis: missing tricuspid valve and Fontan-like circulation

Abstract

Keywords

ASJC Scopus subject areas

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