Abstract
Endomyocardial fibrosis (EMF) is a progressive type of obliterative/restrictive cardiomyopathy characterized by fibrosis of the apical endomyocardium of the ventricles. Although the prognosis of EMF patients is poor in tropical regions, the exact clinical course and pathogenesis of patients with EMF are not known. Here, we report the rare case with EMF in the seventh decade, who showed the disappearance of papillary muscles, chordae tendineae, and part of the tricuspid valves due to massive right ventricular thrombus. Because of those unusual findings of the isolated RV involvement, we observed continuous forward pulmonary artery flow, as occurring in a Fontan circulation.
| Original language | English |
|---|---|
| Pages (from-to) | 1-4 |
| Number of pages | 4 |
| Journal | Heart and Vessels |
| DOIs | |
| Publication status | Accepted/In press - 2016 Jan 8 |
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Keywords
- Endomyocardial fibrosis
- Inflammation
- Prognosis
- Right ventricle thrombus
ASJC Scopus subject areas
- Cardiology and Cardiovascular Medicine
Cite this
Endomyocardial fibrosis : missing tricuspid valve and Fontan-like circulation. / Shiraishi, Yasuyuki; Kohno, Takashi; Nishimura, Yoko; Shimoda, Masayuki; Ikeda, Yoshihiko; Nakajima, Kazuaki; Nishiyama, Takahiko; Nishiyama, Nobuhiro; Murata, Mitsushige; Maekawa, Yuichiro; Sano, Motoaki; Fukuda, Keiichi.
In: Heart and Vessels, 08.01.2016, p. 1-4.Research output: Contribution to journal › Article
}
TY - JOUR
T1 - Endomyocardial fibrosis
T2 - missing tricuspid valve and Fontan-like circulation
AU - Shiraishi, Yasuyuki
AU - Kohno, Takashi
AU - Nishimura, Yoko
AU - Shimoda, Masayuki
AU - Ikeda, Yoshihiko
AU - Nakajima, Kazuaki
AU - Nishiyama, Takahiko
AU - Nishiyama, Nobuhiro
AU - Murata, Mitsushige
AU - Maekawa, Yuichiro
AU - Sano, Motoaki
AU - Fukuda, Keiichi
PY - 2016/1/8
Y1 - 2016/1/8
N2 - Endomyocardial fibrosis (EMF) is a progressive type of obliterative/restrictive cardiomyopathy characterized by fibrosis of the apical endomyocardium of the ventricles. Although the prognosis of EMF patients is poor in tropical regions, the exact clinical course and pathogenesis of patients with EMF are not known. Here, we report the rare case with EMF in the seventh decade, who showed the disappearance of papillary muscles, chordae tendineae, and part of the tricuspid valves due to massive right ventricular thrombus. Because of those unusual findings of the isolated RV involvement, we observed continuous forward pulmonary artery flow, as occurring in a Fontan circulation.
AB - Endomyocardial fibrosis (EMF) is a progressive type of obliterative/restrictive cardiomyopathy characterized by fibrosis of the apical endomyocardium of the ventricles. Although the prognosis of EMF patients is poor in tropical regions, the exact clinical course and pathogenesis of patients with EMF are not known. Here, we report the rare case with EMF in the seventh decade, who showed the disappearance of papillary muscles, chordae tendineae, and part of the tricuspid valves due to massive right ventricular thrombus. Because of those unusual findings of the isolated RV involvement, we observed continuous forward pulmonary artery flow, as occurring in a Fontan circulation.
KW - Endomyocardial fibrosis
KW - Inflammation
KW - Prognosis
KW - Right ventricle thrombus
UR - http://www.scopus.com/inward/record.url?scp=84953383870&partnerID=8YFLogxK
UR - http://www.scopus.com/inward/citedby.url?scp=84953383870&partnerID=8YFLogxK
U2 - 10.1007/s00380-015-0792-8
DO - 10.1007/s00380-015-0792-8
M3 - Article
SP - 1
EP - 4
JO - Heart and Vessels
JF - Heart and Vessels
SN - 0910-8327
ER -