Ewing sarcoma/primitive neuroectodermal tumor of the kidney in a child

Miho Maeda, Akio Tsuda, Shingo Yamanishi, Yoko Uchikoba, Yoshitaka Fukunaga, Hajime Okita, Jun Ichi Hata

Research output: Contribution to journalArticle

12 Citations (Scopus)

Abstract

A 6-year-old female was admitted with abdominal pain and a mass in the right abdomen. Her lactose dehydrogenase level was 1,200 IU/L, and neuron specific enolase was 120 ng/ml. Computed tomography scan confirmed a large right renal mass with necrosis. A right radical nephrectomy was performed. The tumor was completely encapsulated. Based on small round cell histology, strong MIC-2 (CD99) positive tumor cells, and EWS-FLI-1 fusion transcript, Ewing sarcoma/primitive neuroectodermal tumor of the kidney was diagnosed. Induction and follow-up with seven cycles of chemotherapy were given after surgery. She has had no evidence of recurrence 90 months from diagnosis.

Original languageEnglish
Pages (from-to)180-183
Number of pages4
JournalPediatric Blood and Cancer
Volume50
Issue number1
DOIs
Publication statusPublished - 2008 Jan
Externally publishedYes

    Fingerprint

Keywords

  • Electron microscopy
  • Ewing sarcoma/primitive neuroectodermal tumor
  • EWS-FLI-1
  • Immunohistochemistry
  • Kidney

ASJC Scopus subject areas

  • Cancer Research
  • Pediatrics, Perinatology, and Child Health
  • Hematology

Cite this

Maeda, M., Tsuda, A., Yamanishi, S., Uchikoba, Y., Fukunaga, Y., Okita, H., & Hata, J. I. (2008). Ewing sarcoma/primitive neuroectodermal tumor of the kidney in a child. Pediatric Blood and Cancer, 50(1), 180-183. https://doi.org/10.1002/pbc.20831