Abstract
A 6-year-old female was admitted with abdominal pain and a mass in the right abdomen. Her lactose dehydrogenase level was 1,200 IU/L, and neuron specific enolase was 120 ng/ml. Computed tomography scan confirmed a large right renal mass with necrosis. A right radical nephrectomy was performed. The tumor was completely encapsulated. Based on small round cell histology, strong MIC-2 (CD99) positive tumor cells, and EWS-FLI-1 fusion transcript, Ewing sarcoma/primitive neuroectodermal tumor of the kidney was diagnosed. Induction and follow-up with seven cycles of chemotherapy were given after surgery. She has had no evidence of recurrence 90 months from diagnosis.
| Original language | English |
|---|---|
| Pages (from-to) | 180-183 |
| Number of pages | 4 |
| Journal | Pediatric Blood and Cancer |
| Volume | 50 |
| Issue number | 1 |
| DOIs | |
| Publication status | Published - 2008 Jan 1 |
| Externally published | Yes |
Keywords
- EWS-FLI-1
- Electron microscopy
- Ewing sarcoma/primitive neuroectodermal tumor
- Immunohistochemistry
- Kidney
ASJC Scopus subject areas
- Pediatrics, Perinatology, and Child Health
- Hematology
- Oncology
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Cite this
Maeda, M., Tsuda, A., Yamanishi, S., Uchikoba, Y., Fukunaga, Y., Okita, H., & Hata, J. I. (2008). Ewing sarcoma/primitive neuroectodermal tumor of the kidney in a child. Pediatric Blood and Cancer, 50(1), 180-183. https://doi.org/10.1002/pbc.20831