Inner ear salivary gland choristoma extending to the middle ear with congenital profound hearing loss and facial palsy: a case report

Yoshiharu Yamanobe, Naoki Oishi, Takanori Nishiyama, Makoto Hosoya, Kaoru Ogawa

Research output: Contribution to journalArticlepeer-review

Abstract

Background: Salivary gland choristoma (SGCh) is a rare benign tumor reported in several unusual sites, such as the gastrointestinal tract, the optic nerve, and the internal auditory canal, but never reported in the inner ear. Case presentation: An 8-year-old girl with a history of left profound congenital hearing loss presented to us with ipsilateral progressive severe facial nerve palsy (House-Brackmann Grade VI). The left tympanic membrane was swollen with a pulsatile tumor. Radiological investigations revealed a multilocular tumor in the inner ear extending into the middle ear and internal auditory canal (IAC). We performed a partial resection of the tumor by transmastoid approach to preserve the anatomical structure of the facial nerve. The tumor was pathologically diagnosed as SGCh. Two years after surgery, her facial function recovered to House-Brackmann Grade II and the residual tumor did not show regrowth on MRI. Conclusions: Although the natural course of this rare tumor is unknown, a partial resection is an acceptable treatment procedure when functional recovery of the facial nerve is anticipated. Graphical abstract: [Figure not available: see fulltext.]

Original languageEnglish
Article number25
JournalJournal of Otolaryngology - Head and Neck Surgery
Volume50
Issue number1
DOIs
Publication statusPublished - 2021 Dec

Keywords

  • Congenital hearing loss
  • Disequilibrium
  • Inner ear tumor
  • Pediatric ear tumors
  • Pediatric facial palsy
  • Salivary gland choristoma

ASJC Scopus subject areas

  • Surgery
  • Otorhinolaryngology

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