Long-term outcome of fibrous dysplasia

Reconstruction with dysplastic bone

Yoshiaki Sakamoto, Hideo Nakajima, Ikkei Tamada, Kazuo Kishi, Takeshi Kawase

Research output: Contribution to journalArticle

Abstract

A 10-year-old girl presented with facial asymmetry associated with bulging of the right fronto-orbital region with no symptoms. Computed tomography demonstrated enlargement of the right zygomatic, frontal, ethmoid, and sphenoid bones. Abnormal proliferation of the bone had obliterated the sphenoid, right frontal sinus, and right ethmoid sinuses. These radiological findings suggested right optic nerve compression due to fibrous dysplasia. Right optic canal decompression was performed. In preparation for recurrence, the resulting bone defect in the right orbital roof was reconstructed using the outer table of the split lesion bone. The removed frontal bone was divided into intact and lesioned parts, and the intact part was returned. The lesioned part was split and the outer table graft used to reconstruct the frontal region. A temporal musculopericranial flap was used to form a barrier between the opened ethmoid sinus and cranial cavity. A protrusion appeared on the left forehead 10 years later, and was shaved to improve the aesthetic appearance. The patient was followed up for a total of 23 years. The use of dysplastic bone involves the risk of recurrence, but the period of recurrence is delayed and the progression stops after adolescence, so the second operation involved only shaving for aesthetic appearance. This procedure is one of the treatments of choice because of easy reconstruction, easy revision, and good results.

Original languageEnglish
Pages (from-to)857-860
Number of pages4
JournalNeurologia Medico-Chirurgica
Volume51
Issue number12
DOIs
Publication statusPublished - 2011 Dec 25

Fingerprint

Ethmoid Sinus
Frontal Bone
Bone and Bones
Esthetics
Recurrence
Sphenoid Bone
Ethmoid Bone
Facial Asymmetry
Frontal Sinus
Forehead
Optic Nerve
Decompression
Tomography
Transplants
Therapeutics

Keywords

  • Autogenous graft
  • Craniofacial surgery
  • Dysplastic bone
  • Fibrous dysplasia
  • Reconstruction

ASJC Scopus subject areas

  • Clinical Neurology
  • Surgery

Cite this

Long-term outcome of fibrous dysplasia : Reconstruction with dysplastic bone. / Sakamoto, Yoshiaki; Nakajima, Hideo; Tamada, Ikkei; Kishi, Kazuo; Kawase, Takeshi.

In: Neurologia Medico-Chirurgica, Vol. 51, No. 12, 25.12.2011, p. 857-860.

Research output: Contribution to journalArticle

Sakamoto, Yoshiaki ; Nakajima, Hideo ; Tamada, Ikkei ; Kishi, Kazuo ; Kawase, Takeshi. / Long-term outcome of fibrous dysplasia : Reconstruction with dysplastic bone. In: Neurologia Medico-Chirurgica. 2011 ; Vol. 51, No. 12. pp. 857-860.
@article{4377013412b54710b34d03c6dd9fd715,
title = "Long-term outcome of fibrous dysplasia: Reconstruction with dysplastic bone",
abstract = "A 10-year-old girl presented with facial asymmetry associated with bulging of the right fronto-orbital region with no symptoms. Computed tomography demonstrated enlargement of the right zygomatic, frontal, ethmoid, and sphenoid bones. Abnormal proliferation of the bone had obliterated the sphenoid, right frontal sinus, and right ethmoid sinuses. These radiological findings suggested right optic nerve compression due to fibrous dysplasia. Right optic canal decompression was performed. In preparation for recurrence, the resulting bone defect in the right orbital roof was reconstructed using the outer table of the split lesion bone. The removed frontal bone was divided into intact and lesioned parts, and the intact part was returned. The lesioned part was split and the outer table graft used to reconstruct the frontal region. A temporal musculopericranial flap was used to form a barrier between the opened ethmoid sinus and cranial cavity. A protrusion appeared on the left forehead 10 years later, and was shaved to improve the aesthetic appearance. The patient was followed up for a total of 23 years. The use of dysplastic bone involves the risk of recurrence, but the period of recurrence is delayed and the progression stops after adolescence, so the second operation involved only shaving for aesthetic appearance. This procedure is one of the treatments of choice because of easy reconstruction, easy revision, and good results.",
keywords = "Autogenous graft, Craniofacial surgery, Dysplastic bone, Fibrous dysplasia, Reconstruction",
author = "Yoshiaki Sakamoto and Hideo Nakajima and Ikkei Tamada and Kazuo Kishi and Takeshi Kawase",
year = "2011",
month = "12",
day = "25",
doi = "10.2176/nmc.51.857",
language = "English",
volume = "51",
pages = "857--860",
journal = "Neurologia Medico-Chirurgica",
issn = "0470-8105",
publisher = "Japan Neurosurgical Society",
number = "12",

}

TY - JOUR

T1 - Long-term outcome of fibrous dysplasia

T2 - Reconstruction with dysplastic bone

AU - Sakamoto, Yoshiaki

AU - Nakajima, Hideo

AU - Tamada, Ikkei

AU - Kishi, Kazuo

AU - Kawase, Takeshi

PY - 2011/12/25

Y1 - 2011/12/25

N2 - A 10-year-old girl presented with facial asymmetry associated with bulging of the right fronto-orbital region with no symptoms. Computed tomography demonstrated enlargement of the right zygomatic, frontal, ethmoid, and sphenoid bones. Abnormal proliferation of the bone had obliterated the sphenoid, right frontal sinus, and right ethmoid sinuses. These radiological findings suggested right optic nerve compression due to fibrous dysplasia. Right optic canal decompression was performed. In preparation for recurrence, the resulting bone defect in the right orbital roof was reconstructed using the outer table of the split lesion bone. The removed frontal bone was divided into intact and lesioned parts, and the intact part was returned. The lesioned part was split and the outer table graft used to reconstruct the frontal region. A temporal musculopericranial flap was used to form a barrier between the opened ethmoid sinus and cranial cavity. A protrusion appeared on the left forehead 10 years later, and was shaved to improve the aesthetic appearance. The patient was followed up for a total of 23 years. The use of dysplastic bone involves the risk of recurrence, but the period of recurrence is delayed and the progression stops after adolescence, so the second operation involved only shaving for aesthetic appearance. This procedure is one of the treatments of choice because of easy reconstruction, easy revision, and good results.

AB - A 10-year-old girl presented with facial asymmetry associated with bulging of the right fronto-orbital region with no symptoms. Computed tomography demonstrated enlargement of the right zygomatic, frontal, ethmoid, and sphenoid bones. Abnormal proliferation of the bone had obliterated the sphenoid, right frontal sinus, and right ethmoid sinuses. These radiological findings suggested right optic nerve compression due to fibrous dysplasia. Right optic canal decompression was performed. In preparation for recurrence, the resulting bone defect in the right orbital roof was reconstructed using the outer table of the split lesion bone. The removed frontal bone was divided into intact and lesioned parts, and the intact part was returned. The lesioned part was split and the outer table graft used to reconstruct the frontal region. A temporal musculopericranial flap was used to form a barrier between the opened ethmoid sinus and cranial cavity. A protrusion appeared on the left forehead 10 years later, and was shaved to improve the aesthetic appearance. The patient was followed up for a total of 23 years. The use of dysplastic bone involves the risk of recurrence, but the period of recurrence is delayed and the progression stops after adolescence, so the second operation involved only shaving for aesthetic appearance. This procedure is one of the treatments of choice because of easy reconstruction, easy revision, and good results.

KW - Autogenous graft

KW - Craniofacial surgery

KW - Dysplastic bone

KW - Fibrous dysplasia

KW - Reconstruction

UR - http://www.scopus.com/inward/record.url?scp=84455181447&partnerID=8YFLogxK

UR - http://www.scopus.com/inward/citedby.url?scp=84455181447&partnerID=8YFLogxK

U2 - 10.2176/nmc.51.857

DO - 10.2176/nmc.51.857

M3 - Article

VL - 51

SP - 857

EP - 860

JO - Neurologia Medico-Chirurgica

JF - Neurologia Medico-Chirurgica

SN - 0470-8105

IS - 12

ER -