Primary surgical repair of aorticopulmonary septal defect with coarctation of the aorta

Two infants with aorticopulmonary septal defect (APSD) and coarctation of the aorta (CoA) underwent primary surgical repair and their aortic arches were reconstructed in a manner of end-to-end anastomosis. One of the cases, 4-day-old girl and Type I of Mori's classification, underwent Sandwich patch closure of the communicating vessel. The other, 40-day-old girl and Type III, underwent division of he communicating vessel. Aortic wall was primarily closed and pulmonary artery was reconstructed with a pericardial patch. Both survived the surgery, and are well without medication at 13 and 14 postoperative months. Interrupted aortic arch is commonly known as the associated aortic arch anomaly of APSD, and to the best of our knowledge, this is the first report of CoA as the associated anomaly of APSD. Whichever the anomaly of the aortic arch, early diagnosis and primary surgical repair in the early ages are urgently needed for favorable outcome of the patient.