Successful Total Pericardiectomy for Constrictive Pericarditis in the First Series of Japanese Patients With Mulibrey Nanism

Jun Yasuhara, Sayu Omori, Jun Maeda, Naomi Nakagawa, Masahiro Kamada, Kenjiro Kosaki, Ryo Aeba, Hiroyuki Yamagishi

Research output: Contribution to journalArticle

2 Citations (Scopus)

Abstract

Patients with Mulibrey nanism (MUL) present with growth failure and multiple organ manifestations, and MUL is caused by mutations in TRIM37. In this article, we report on the first case series of Japanese patients with MUL who developed congestive heart failure due to constrictive pericarditis. Our case series suggests that early diagnosis and total pericardiectomy before adherence of the pericardium might provide clinical benefit and better prognosis for MUL.

Original languageEnglish
Pages (from-to)690.e5-690.e8
JournalCanadian Journal of Cardiology
Volume34
Issue number5
DOIs
Publication statusPublished - 2018 May 1

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine

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